Background: Klatskin tumor (hilar cholangiocarcinoma or central bile duct carcinoma, KCC) is a rare type of tumor, with an annual incidence of no more than 1: 100 000. It originates from the bifurcation of the extrahepatic bile duct and was first described in 1965 by Gerald Klatskin who reported 15 cases and defined some features in this cholangiocarcinoma. Most KCCs are adenocarcinomas with poor differentiation degree,spreading along the duct and nerve sheath.

Klatskin tumor, choledochectomy, gamma-glutamyl transpeptidase, Jaundice, Hepatic cholangiocarcinoma